Test Category: Immunology
Investigation Name:Proteinase 3 antibody (PR3)

Alias or Abbreviation:PR3, ANCA
Intro:
Indication: Granulomatosis with polyangiitis (GPA, formerly called Wegener's granulomatosis) Further information: In accordance with the revised 2017 international consensus on testing of ANCAs, ANCA requests should be confined to patients with a high pre-test probability of small vessel vasculitis, if misleading 'false positives' in a range of non-vasculitic disorders are to be avoided. Indications are: • Glomerulonephritis, especially rapidly progressing glomerulonephritis • Pulmonary haemorrhage, especially pulmonary renal syndrome • Acute pulmonary-renal syndrome • Cutaneous vasculitis with systemic features • Multiple lung nodules • Chronic destructive disease of the upper airways • Long-standing sinusitis or otitis • Granulomatous nasopharyngeal lesions • Subglottic tracheal stenoses • Mononeuritis multiplex, or other peripheral neuropathy • Retro-orbital mass • Scleritis Antibodies to PR3 are highly sensitive and specific for GPA. The sensitivity is dependent on the phase and on the activity of the disease. PR3 antibodies may also be seen in MPA and EGPA. PR3 antibodies may also occur in 20% to 30% of patients with necrotizing glomerulonephritis with no obvious extrarenal manifestations of small vessel vasculitis. NOTE: Results >2.0 IU/mL are reflexed for ANCA test on new patients only For urgent requests, contact the Laboratory directlyRequestable Seperately?No
Minimum Sample Volume:1mL
Expected Turnaround Time:Frequency: Daily Target: 3 days
Test Code:ANCA
Sample Type:
Serum Gel Tube (Gold top)/ PlasmaComplex Reference Range:<2 IU/mL = Negative
Collection Conditions / Other Information:1st class post or Transport
Referred to Another Laboratory?No
Storage Requirements:Ambient temperature
NPEX / PDF Reporting Available:Yes
EQA Scheme:Yes
Further information:Orderable in panel with MPO
Lead Contact Details:rwh-tr.bcpsimmunologyclinicalqueries@nhs.net
Email Address For Chasing Results:rwh-tr.ImmunologyLab@nhs.net
Methodology:Fluoroenzymeimmunoassay
UKAS Reference Number:9580 (recommended)
Site Sample Tested:Immunology, New Cross Hospital, Wolverhampton